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The Cerebral Cortex


The Spinal Cord | The Brain Stem And Cerebellum | The Diencephalon | The Basal Ganglia | The Cerebral Cortex | The Peripheral Nervous System, Neuromuscular Junction, and Muscle

The primary sensory and motor areas

You should know where primary visual, auditory, somatosensory and motor cortices are located:See figure 15.

  1. The visual (striate) cortex (calcarine cortex, occipital lobes, area 17) Take time to review the visual pathways: retina optic nerve optic chiasm optic tract lateral geniculate body optic radiations visual cortex). Note that anterior to the optic chiasm, unilateral lesions produce visual deficits in only one eye, whereas posterior to the chiasm, deficits are restricted to one visual field (but are present in both eyes). See figure 11.
  2. The auditory cortex (Heschl's gyrus, temporal lobe, within the Sylvian fissure).
  3. The somatosensory cortex (post-central gyrus, areas 3,1 and 2).
  4. The motor cortex (pre-central gyrus, area 4).

Association cortex:

  1. Unimodal association cortex: Each of the primary sensory cortices is bordered by unimodal association cortex (that is, with direct connections to only one sensory modality).
  2. Polymodal and supramodal association cortices are interconnected with unimodal association areas as well as other higher-order association cortices. Function is thought to depend upon complex networks of neurons in multiple regions; nevertheless, very specific functions are subserved by different regions. Some regions are specialized for specific language functions, others for visuospatial, etc.
  3. Prefrontal cortex: The expanse of cortex anterior to the motor and pre-motor areas subserves Aexecutive@ functions. Patients with frontal lobe damage may have difficulty using information not immediately at hand to direct behavior. They therefore exhibit poor planning and judgement (see below).

Cerebral dominance

The two cerebral hemispheres are not functionally equivalent. The following functional asymmetries have been well-documented:

Language
In over 95% of right-handers, the left hemisphere is dominant for language. In left handers, either left hemisphere dominance or bilateral language capabilities are the commonest findings; right hemisphere dominance is also described.
Handedness/praxis
Handedness reflects a functional hemispheric asymmetry for fine motor ability. Limb apraxia results from damage to the hemisphere opposite the dominant hand (e.g., the left hemisphere, in right-handers).
Attention
Severe unilateral neglect is seen much more often with right than with left hemisphere damage, reflecting (it is thought) a functional hemispheric asymmetry of attentional mechanisms.
Visuospatial abilities
Certain visuospatial skills are more highly developed in the right hemisphere.
Emotion
While the exact nature of this asymmetry remains to be defined, the emotional effects of left hemisphere damage appear to be different from those of right hemisphere damage. Left frontal lesions are more likely to be associated with depression, whereas right hemisphere damage is more likely to cause emotional flattening.

Limbic cortex: emotion and memory.

Anatomy (see figure 16)

Limbus means rim. Structures of the limbic cortex form a ring around the brainstem and diencephalon. Limbic structures include (going in a circle) the amygdala, hippocampus and parahippocampal gyrus, cingulate cortex, orbitofrontal, and insular cortex. Limbic regions tend to have a more primitive structure than neocortex, and are highly interconnected with basal forebrain and hypothalamus.

Function:

Emotion
Emotional behavior entails endocrine, autonomic and motor changes regulated by the hypothalamus. Because the limbic forebrain is interposed between neocortex and hypothalamus, it is logical to suppose that it mediates cortical influence over hypothalamic function. Clinical and experimental data confirms this for a portion of the limbic forebrain: in animals, lesions of the orbitofrontal and temperopolar cortex, and of the amygdala, are associated with changes in emotional behavior. In humans, seizures arising from medial temporal structures (especially the amygdala) can be manifested by emotional feelings such as fear.
Memory
Lesions affecting the hippocampus and its connections do not appear to affect emotions, but instead can profoundly affect memory. Discrete lesions in the following structures can cause isolated and profound memory disturbances:
  • the hippocampus and adjacent temporal cortex (entorhinal and perirhinal cortex).
  • the medial thalamus (anterior thalamus, mamillothalamic tract, dorsomedial thalamus)
  • the basal forebrain, perhaps especially the cholinergic neurons of the septal nuclei the diagonal band of Broca that project to the hippocampus. Other structures in this complex area may also contribute to memory.

    Clinical syndromes

    Only a few will be mentioned.

    The Aphasias (see Figure 17)

    Aphasia is most often associated with damage to left hemisphere cortex. The following distinctions are useful:

    Summary of the aphasias
    Syndrome Spont. Speech Comprehension Repetition Naming
    Perisylvian aphasias
    Broca's Non-fluent ("Telegraphic") Good Poor Poor
    Wernicke's Fluent (phonemic paraphasias) Poor Poor Poor
    Conduction Fluent (phonemic paraphasias) Good Poor Poor
    Global Non-fluent Poor Poor Poor
    Trans-cortical aphasias
    Transcortical motor Non-fluent Good Good Var.
    Transcortical sensory Fluent (semantic paraphasias) Poor Good Poor
    Mixed Transcortical Non-fluent Poor Good Poor
    Anomic Fluent (circumlocution..) Good Good Poor


    The peri-sylvian aphasias

    Structures around the sylvian fissure mediate auditory language repetition. Auditory signals are processed by Heschl's gyrus (primary auditory cortex), and phonemic analysis probably takes place in the adjacent auditory association cortex (Wernicke's area). Speech is encoded by more anterior regions (among them, Broca's area, in front of the motor cortex), and these regions direct the adjacent motor cortex to produce the appropriate movements. Damage to any of these regions impairs language repetition, the hallmark of the perisylvian aphasias. Language comprehension requires that the phonetically analyzed information be communicated to regions outside the perisylvian region (among them, the angular gyrus).

    Broca's aphasia
    Characterized by non-fluent speech, poor repetition and relatively spared comprehension. Lesions are in Broca's area and adjacent cortex.
    Wernicke's aphasia
    Fluent, but nonsensical speech with phonemic paraphasias (substitution of incorrect sounds), and impaired repetition and comprehension. Lesions are in Wernicke's area.
    Conduction aphasia
    Fluent speech, spared comprehension, and poor repetition. Lesions may disconnect Wernicke's from Broca's area.
    Global aphasia
    Non-fluent speech, poor repetition and poor comprehension. The entire perisylvian cortex is involved.

    The transcortical aphasias

    These are characterized by intact repetition. Lesions are more varied than with perisylvian aphasias. In addition to the cortical localizations noted, transcortical aphasias may result from subcortical damage.

    Transcortical motor aphasia
    Speech is non-fluent, but repetition and comprehension are spared. Lesions are frontal, but spare Broca's area.
    Transcortical sensory aphasia
    Speech is fluent, but empty, and often semantic paraphasias (substitutions of incorrect words) are found. Comprehension is impaired, but repetition is normal. Lesions are posterior, but spare Wernicke's area.
    Anomic aphasia
    This can be conceived of as a mild transcortical sensory aphasia, in which comprehension is not affected, but naming is impaired. Speech is fluent, with circumlocution (when the patient cannot find a word). Repetition is normal. Angular and middle temporal gyrus lesions, as well as other areas, have been implicated.
    Mixed transcortical aphasia
    Non-fluent speech, with poor comprehension, but normal repetition. Patients may echo fragments of other's speech (echolalia). Lesions usually encompass thos of both transcortical motor and transcortical sensory aphasias, and are most often from watershed infarctions associated with severe carotid artery stenosis.

    Disconnection syndromes

    Neurological deficits may result not only from destruction of cortical regions that subserve specific functions, but also from disconnections between these areas. An example is the syndrome of alexia without agraphia (pure word blindness, Djerine's syndrome). Most commonly caused by left posterior cerebral artery territory infarction, the lesion disconnects the right visual cortex from the left hemisphere language centers. The left visual cortex is destroyed. The patient cannot read in the intact left visual field, but other language functions are normal. See figure 18.

    Unilateral neglect

    Patients fail to respond, or respond more slowly, to stimuli presented in the field opposite the lesion. They may initially appear hemianopic, or hemianesthetic, but eventually it can be shown that sensory function is normal, if their attention can be maintained. Patients may also have anosognosia: failure to recognize their deficits. They may explicitly deny a hemiplegia, or fail to recognize that they have had a stroke. Neglect is more frequent and more severe with right than with left hemisphere lesions.

    The amnesic syndrome

    The core features of the amnesic syndrome are: (1) Anterograde amnesia, an inability to learn new information after the onset of amnesia. (2) Retrograde amnesia, an inability to retrieve information that was learned prior to the onset of amnesia. (3) Normal attention and intellectual function: Many amnesics have normal language, praxis, visuospatial, and even frontal lobe function. Unless you specifically test memory, they may appear to be normal. Furthermore, certain kinds of memory are spared in the amnesic syndrome: patients can learn routines such as motor skills, and mirror reading; their behavior may be influenced by information that they cannot consciously recall. These spared functions are thus mediated by different brain structures. It is thought, for example, that motor memories and habits may be mediated through the basal ganglia, but this remains to be clarified. Diseases associated with the amnesic syndrome include stroke or tumor, if any of the critical areas is affected, head injury, Wernicke-Korsakoff disorder from thiamine deficiency, and Alzheimer's disease (which affects the hippocampus and basal forebrain). In Alzheimer's disease, cognitive deficits (aphasia, apraxia, visuospatial disorders) soon combine with amnesia to produce a more complex clinical picture.

    Frontal lobe syndromes

    The frontal lobes have a high-order executive role in behavior. Without their guidance, we are left at the mercy of immediate stimuli. Frontal patients may therefore demonstrate stimulus-bound behavior: they may use available objects even when there is no reason to do so (utilization behavior), they perseverate (re-use the most recent responses), and they do not seek understanding beyond what is most obvious. They may demonstrate pseudopsychopathic behavior, failing to consider the consequences of their actions, making irresponsible decisions in business, and at times making inappropriate sexual advances (despite often overall reduced libido). Patients with frontal dementias also fail to organize their experience, and do not plan for the future. They often forget things, not because they cannot encode new memories, but because they fail to initiate memory searches when appropriate. For example, the patient may be told to go to the store to buy five items, but when he gets to the store he is attracted to a magazine, reads it, and then comes home with nothing. When asked why he was sent to the store, he can recall the items he was supposed to have purchased; he just forgot to remember them when it was appropriate. [The patient with the classical amnesic syndrome would not recall the list after distraction.] Patients with orbitofrontal lesions appear to have most difficulty inhibiting inappropriate behavior. Patients with medial lesions tend to be akinetic, and fail to initiate behavior.


      Updated: December 23, 2003
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